網膜色素変性症
WordNet
- a special situation; "this thing has got to end"; "it is a remarkable thing"
- a separate and self-contained entity
- an action; "how could you do such a thing?"
- an artifact; "how does this thing work?"
- an entity that is not named specifically; "I couldnt tell what the thing was"
- any attribute or quality considered as having its own existence; "the thing I like about her is ..."
- a persistent illogical feeling of desire or aversion; "he has a thing about seafood"; "she has a thing about him"
- a special abstraction; "a thing of the spirit"; "things of the heart"
- a special objective; "the thing is to stay in bounds"
- a statement regarded as an object; "to say the same thing in other terms"; "how can you say such a thing?"
- an event; "a funny thing happened on the way to the..."
- the process of declining from a higher to a lower level of effective power or vitality or essential quality (同)devolution
- passing from a more complex to a simpler biological form (同)retrogression
- the innermost light-sensitive membrane covering the back wall of the eyeball; it is continuous with the optic nerve
PrepTutorEJDIC
- 〈C〉(形のある)『物』,物体;(生物に対しての)『無生物』 / 〈C〉(形のない)『もの』,事,事柄,でき事 / 《複数形で》事情,事態,状勢,状況 / 《複数形で》(すべての)事物,事柄 / 《通例 the~》(努力・活動などの)目的,目標 / 〈C〉衣服,衣類・《one's things》持ち物,所持品,身の回り品 / 《複数形で》道具,用具・〈C〉《親愛・哀れみ・軽べつなどの感情をこめて》人,者,やつ / 《the~》《話》(…の)流行《+in+名》
- 《所有・所属》…『の』,…のものである,…に属する・《材料・要素》…『でできた』,から成る・《部分》…『の』[『中の』] ・《数量・単位・種類を表す名詞に付いて》…の・《原因・動機》…『で』,のために(because of) ・《主格関係》…『の』,による,によって・《目的格関係》…『を』,の・《同格関係》…『という』・《関係・関連》…『についての』[『の』],の点で・《抽象名詞などと共に》…の[性質をもつ] ・《『It is』+『形』+『of』+『名』+『to』 doの形で,ofの後の名詞を意味上の主語として》・《分離》…『から』・《起原・出所》…『から』[『の』](out of) ・《『名』+『of』+『a』(『an』)+『名』の形で》…のような・《『名』+『of』+『mine』(『yours, his』など独立所有格)の形で》…の…・《時》(1)《副詞句を作って》…に《形容詞句を作って》…の・《時刻》《米》…前(to,《米》before)
- 《前述の名詞または文脈でそれと分かる名詞に付けて》『その』,あの,名の / 《唯一の事物に付けて》 / 《方角・自然現象に付けて》 / 《用具・楽器・特定の病気などに付けて》 / 《修飾吾[句]を伴う名詞に付けて》 / 《単数普通名詞に付けて》(1)《種族全体》…『というもの』 / 《複数名詞または集合名詞に付けて》 / 《単位》『…につき;…単位[で]』 / 《身体の一部に付けて,所有格に代わる》 / 《形容詞に付けて》 / 《固有名詞に付けて》 / 《強意用法に》『随一の』,典型的な / 《「the+比較級,the+比較級」の形で》『…すればするほどそれだけ』 / 《比較級の前に》(…につれて,のために)『それだけ』,ますます
- 退歩,退化,墜落
- (目の)網膜
UpToDate Contents
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- 1. 加齢黄斑変性：臨床像、病因、および診断 age related macular degeneration clinical presentation etiology and diagnosis
- 2. 加齢黄斑変性：治療および予防 age related macular degeneration treatment and prevention
- 3. 肝斑 melasma
- 4. 皮膚扁平上皮癌の疫学および危険因子 epidemiology and risk factors for cutaneous squamous cell carcinoma
- 5. 色素沈着過剰を有する患者へのアプローチ approach to the patient with hyperpigmentation disorders
English Journal
- SEGREGATION OF OPHTHALMOSCOPIC CHARACTERISTICS ACCORDING TO CHOROIDAL THICKNESS IN PATIENTS WITH EARLY AGE-RELATED MACULAR DEGENERATION.
- Switzer DW Jr, Mendonça LS, Saito M, Zweifel SA, Spaide RF.SourceVitreous, Retina, Macula Consultants of New York and the LuEsther T. Mertz Retinal Research Center, Manhattan Eye, Ear and Throat Hospital, New York, New York.
- Retina (Philadelphia, Pa.).Retina.2012 Jan 4. [Epub ahead of print]
- PURPOSE: To investigate the association of fundus features with choroidal thickness in eyes with early age-related macular degeneration.METHODS: Consecutive patients with age-related macular degeneration were evaluated. Major exclusionary criteria included late age-related macular degeneration (cent
- PMID 22222760
- RANDOMIZED CLINICAL TRIAL FRANCE DMLA2: Effect of Trimetazidine on Exudative and Nonexudative Age-Related Macular Degeneration.
- Cohen SY, Bourgeois H, Corbe C, Chaine G, Espinasse-Berrod MA, Garcia-Sanchez J, Gaudric A, Hullo A, Leys A, Soubrane G, Sahel JA.SourceFrom the *Ophthalmic Center for Imaging and Laser, Paris, France; †Val de Gràce Hospital, Paris, France; ‡Invalids Hospital, Paris, France; §Avicenne Hospital, Bobigny, France; Necker Hospital, Paris, France; **San Carlos Clinical Hospital, Complutense University of Madrid, Madrid, Spain; ††Lariboisiere Hospital, Paris, France; ‡‡Lyon-Sud Hospital, France; §§University of Leuven, Belgium; University Eye Clinic, Creteil, France; and ***XV-XX Hospital, Paris, France.
- Retina (Philadelphia, Pa.).Retina.2011 Aug 4. [Epub ahead of print]
- PURPOSE: To evaluate the effect of trimetazidine (TMZ) in a randomized, double-blind, placebo-controlled clinical trial on the occurrence of choroidal neovascularization or geographic atrophy in age-related macular degeneration.METHODS: A total of 1,086 patients from France, Belgium, and Spain with
- PMID 21822162
- Ophthalmic manifestations and histopathology of xeroderma pigmentosum: two clinicopathological cases and a review of the literature.
- Ramkumar HL, Brooks BP, Cao X, Tamura D, Digiovanna JJ, Kraemer KH, Chan CC.SourceImmunopathology Section, Laboratory of Immunology, National Eye Institute, National Institutes of Health, Bethesda, Maryland, USA.
- Survey of ophthalmology.Surv Ophthalmol.2011 Jul-Aug;56(4):348-61. doi: 10.1016/j.survophthal.2011.03.001.
- Xeroderma pigmentosum is a rare, autosomal recessive disease caused by a defect in DNA repair. Patients with xeroderma pigmentosum often have cutaneous and ocular sun sensitivity, freckle-like skin pigmentation, multiple skin and eye cancers, and, in some patients, progressive neurodegeneration. Xer
- PMID 21684361
Japanese Journal
- 眼球の自由運動による眼電位図(EOG)時間曲線の測定
- 伊月 宣之,久保 賢倫,西川 [ヨシ]一
- 電子情報通信学会技術研究報告. MBE, MEとバイオサイバネティックス 97(215), 39-44, 1997-07-26
- ヒトの眼球周辺から導出される電位を記録した眼電位図は, 眼球運動の機能検査や網膜など眼球後極部の電気生理学的な検査法として臨床診断に応用されている. 色素変性症や卵黄様黄斑変性症の診断に有用な眼電位図(EOG)時間曲線は, 視標を目安にして眼球を一定の振幅で左右へ交互にステップ状の衝動運動を起こさせる必要があるため. 視力障害のある者では検査ができない. このような従来の検査法の欠点を改良して, …
- NAID 110003286768
- Pigmentary degeneration induced by N-methyl-N-nitrosourea and the fate of pigment epithelial cells in the rat retina
- NAKAJIMA Motomaro,NAMBU Hiroyuki,SHIKATA Nobuaki,SENZAKI Hideto,MIKI Hirohiko,TSUBURA Airo
- Pathology international 46(11), 874-882, 1996-11
- NAID 10008336096
- 弱視聾(唖)児に対する教育の試み:網膜色素変性による学習障害を伴う視覚, 聴覚重複障害児生徒の事例
Related Links
- This is a rare syndrome consisting of a pigmentary degeneration of the retina in association with nanophthalmos. The globe is small with a thickened choroid and sclera and the macula becomes atrophic later in life. Some patients ...
- What is Pigmentary Degeneration of the Retina? Macular degeneration is a medical condition predominantly found in elderly adults in which the center of the inner lining of the eye, known as the macula area of the retina, suffers ...
★リンクテーブル★
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- 英
- pigmentary degeneration of the retina
- ラ
- degeneratio pigmentosa retinae, retinitis pigmentosa
- 関
- 網膜色素変性、色素性網膜症、色素性網膜炎、桿体錐体ジストロフィー、色素上皮網膜変性、夜盲症、難病
[show details]
概念
遺伝形式
症状
- 症状は通常両眼性である。進行は緩徐に進行する。
- 夜盲
- 視野狭窄：輪状暗点(初期)、求心性視野狭窄(末期)
- 視力低下：周辺視力低下、最終的には失明、。
検査
- 眼底検査：網膜動脈狭細化、蝋状の視神経乳頭萎縮、骨小体様色素沈着(必ずしも見られない)
- 傾向眼底検査
- 暗順応検査
- 網膜電図：(初期から見られる)振幅低下・消失
- 視野検査：(初期)輪状暗点、求心性視野狭窄
認定基準
- 参考1
-
- 網膜血管狭小
- 粗糙胡麻塩状網膜(ごま塩眼底？？)
- 骨小体様色素沈着
- 白点状
- 2) 網膜電図の振幅低下又は消失
- 3) 蛍光眼底造影所見で網膜色素上皮萎縮による過蛍光
合併症
網膜色素変性を伴う疾患
網膜色素変性の類変疾患(網脈絡膜変性疾患)
- →網脈絡膜ジストロフィー
参考
- http://www.nanbyou.or.jp/entry/337
- http://homepage1.nifty.com/jibiaka50/nantyoumoumaku.htm
- 3. [charged] Retinitis pigmentosa: Clinical presentation and diagnosis - uptodate [1]
国試
[★]
- 関
- degeneracy、degenerate、degenerative、denaturation、denature、involution、retract、retrograde degeneration、retrograde degradation、unfolding
[★]
[★]
- 関
- pigmented