parahemophilia

出典: meddic

パラ血友病血友病類似症

factor V deficiency


coagulation factors, fac tor V deficiency

英文文献

  • Platelets and platelet-derived factor Va confer hemostatic competence in complete factor V deficiency.
  • Bouchard BA1, Chapin J1, Brummel-Ziedins KE1, Durda P2, Key NS3, Tracy PB1.
  • Blood.Blood.2015 Jun 4;125(23):3647-50. doi: 10.1182/blood-2014-07-589580. Epub 2015 Apr 20.
  • Whole genome sequencing of an individual completely devoid of plasma- and platelet-derived factor V (FV) identified 167 variants in his F5 gene including previously identified and damaging missense mutations at rs6027 and Leu90Ser. Because the administration of fresh frozen plasma (FFP) prevents gas
  • PMID 25896652
  • Recurrent hemoperitoneum secondary to haemorrhage from the corpus luteum unmasks factor V deficiency.
  • Badyal RK1, Jain K, Mandrelle K, John MJ, Kakkar N, Bose SK, Kumar N, Ahluwalia J.
  • Blood coagulation & fibrinolysis : an international journal in haemostasis and thrombosis.Blood Coagul Fibrinolysis.2015 Apr 17. [Epub ahead of print]
  • Factor V deficiency is a rare autosomal recessive coagulation disorder. We report a case with inherited factor V deficiency presenting as life-threatening recurrent hemoperitoneum, following bleeding from ruptured corpus haemorrhagicum. Prolonged prothrombin and activated partial thromboplastin time
  • PMID 25886835
  • Acquired factor V deficiency in myeloproliferative neoplasms: a Mayo Clinic series of 33 patients.
  • Ashrani AA1, Tefferi A, Pruthi RK, Pardanani A.
  • British journal of haematology.Br J Haematol.2015 Apr 8. doi: 10.1111/bjh.13438. [Epub ahead of print]
  • PMID 25854415

和文文献

  • 先天性第V因子欠乏症を伴う結腸癌の1例
  • 坂田 好史,三島 秀雄,山口 和哉,平林 直樹
  • 日本消化器外科学会雑誌 36(11), 1626-1629, 2003-11-01
  • 症例は71歳の女性で.1999年4月頃から近医で貧血症と便潜血陽性を指摘され当科へ紹介された.両親がいとこ同士の結婚であった.注腸造影検査で肝彎曲部に陰影欠損像を認めた.大腸内視鏡検査では肝彎曲節に1型腫瘍を認めた.入院時検査所見ではプロトロンビン時間(PT)22.8秒(23.5%),活性化部分トロンボプラステン時間(APTT)58.1秒と延長していた.出血時間は2分,ヘパプラスチンテストは98. …
  • NAID 110001294749
  • A Case of Colon Cancer with Congenital Factor V Deficiency
  • 坂田 好史,三島 秀雄,山口 和哉,平林 直樹
  • 日本消化器外科学会雑誌 36(11), 1626-1629, 2003
  • … We found the patient had congenital factor V deficiency (parahemophilia), so we transfused 6 units of fresh frozen plasma (FFP) preoperatively to improve PT and APTT. …
  • NAID 130004343876
  • 先天性第5因子欠之症(Parahemophilia)の1例

関連リンク

parahemophilia par·a·he·mo·phil·i·a (pār'ə-hē'mə-fĭl'ē-ə, -fēl'yə) n. A congenital deficiency of factor V characterized by abnormally slow blood coagulation. Also called Owren's disease.
parahemophilia [par″ah-he″mo-fil´e-ah] a hereditary hemorrhagic tendency due to deficiency of coagulation factor V. Called also Owren's disease. See also clotting. parahemophilia /para·he·mo·phil·ia/ (-he″mo-fil´e-ah) a hereditary ...

関連画像

 Deficiency; Owren Disease; Parahemophilia Deficiency; Owren Disease; Parahemophilia Deficiency; Owren Disease; Parahemophilia Deficiency (Owren Disease; Parahemophilia Deficiency; Owren Disease; ParahemophiliaWhat is para - hemophilia


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リンク元パラ血友病」「血友病類似症

パラ血友病」

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parahemophilia
血友病類似症
-先天性第V因子欠乏症


血友病類似症」

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parahemophilia
第V因子欠乏症パラ血友病




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