小口症
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出典(authority):フリー百科事典『ウィキペディア(Wikipedia)』「2012/05/30 23:25:18」(JST)
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Microstomia |
Classification and external resources |
ICD-10 |
Q18.5 |
ICD-9 |
744.84 |
DiseasesDB |
29609 |
eMedicine |
ent/148 |
MeSH |
D008865 |
Microstomia (micro- a combining form meaning small + -stomia a combining form meaning mouth = (abnormally) "small mouth") is a clinical feature of many craniofacial syndromes, including Freeman-Sheldon syndrome and Sheldon-Hall syndromes (or distal arthrogryposis multiplex congenita). It may present with whistling-face feature, as well, as in Freeman-Sheldon syndrome. In this syndrome, it impairs alimentation and may require repeated oral surgeries (called commissurotomy) to improve function. It can also be a feature of systemic scleroderma.
Congenital malformations and deformations of face and neck (Q18, 744.4–744.9)
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Face |
jaw: Otocephaly
mouth: Macrostomia · Microstomia
lip: Macrocheilia · Microcheilia
chin: Microgenia
multiple/other: Hallermann–Streiff syndrome · Branchial cleft cyst
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Neck |
Webbed neck
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Ungrouped |
Preauricular sinus and cyst
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noco/cofa(c)/cogi/tumr, sysi
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UpToDate Contents
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English Journal
- Epidermolysis Bullosa Oropharyngeal Severity (EBOS) score: A multicenter development and reliability assessment.
- Fortuna G, Chainani-Wu N, Lozada-Nur F, Aria M, Cepeda-Valdes R, Pollio A, Marinkovich MP, Martinez-Salazar AE, Mignogna MD, Bruckner AL, Salas-Alanís JC.SourceDepartment of Dermatology, Stanford University School of Medicine, Center for Clinical Sciences Research, Stanford, California; Oral Medicine Unit, Department of Odontostomatological and Maxillofacial Sciences, Federico II University of Naples, Naples, Italy; DebRA (Dystrophic Epidermolysis Bullosa Research Association) Mexico Foundation, Monterrey, Mexico. Electronic address: giulio.fortuna@gmail.com.
- Journal of the American Academy of Dermatology.J Am Acad Dermatol.2013 Jan;68(1):83-92. doi: 10.1016/j.jaad.2012.04.009. Epub 2012 May 8.
- BACKGROUND: Epidermolysis bullosa (EB) is a genetic mucocutaneous disorder characterized by blister formation upon mild trauma. All 4 EB types may show oropharyngeal lesions involving either hard or soft tissues. Currently, there are very few data on EB scoring that include the oropharyngeal cavity.
- PMID 22575158
- Oro-palatal dysplasia Bettex-Graf - Clinical findings, genetic background, treatment.
- Janiszewska-Olszowska J, Gawrych E, Dydyk A, Studniak E, Biaduń-Popławska A, Zajączek S.SourceDepartment of General Dentistry (Head: Prof. Elżbieta Weyna), Pomeranian Medical University, Al. Powstancow Wlkp. 72, 70-111 Szczecin, Poland. Electronic address: jjo@sci.pam.szczecin.pl.
- Journal of cranio-maxillo-facial surgery : official publication of the European Association for Cranio-Maxillo-Facial Surgery.J Craniomaxillofac Surg.2013 Jan;41(1):e29-32. doi: 10.1016/j.jcms.2012.06.002. Epub 2012 Jul 24.
- Oro-palatal dysplasia Bettex-Graf is an extremely rare syndrome consisting of microstomia, U-shaped cleft palate and micrognathia. Only two affected families have been reported before. We present the clinical findings, treatment and 13 year follow-up in a patient with this rare syndrome. The possibl
- PMID 22831831
- Freeman-Sheldon syndrome: Combined surgical and non-surgical approach.
- Sadrimanesh R, Hassani A, Vahdati SA, Chaghari H, Sadr-Eshkevari P, Rashad A.SourcePrivate Practice, Oral and Maxillofacial Prosthodontist and Implantologist, Tehran, Iran.
- Journal of cranio-maxillo-facial surgery : official publication of the European Association for Cranio-Maxillo-Facial Surgery.J Craniomaxillofac Surg.2012 Dec 3. pii: S1010-5182(12)00243-0. doi: 10.1016/j.jcms.2012.11.004. [Epub ahead of print]
- BACKGROUND: Many Freeman-Sheldon syndrome patients suffer from extensive microstomia resulting in possible inhibition of dental and skeletal development as well as difficulties in eating, speech and dental hygiene. Oral commissure contraction treatments vary from patient education to complicated sur
- PMID 23218872
Japanese Journal
- 反復性口腔内アフタにより小口症をきたした2症例の経験
- 佐藤 秀吉,鳥山 和宏,八木 俊路朗,中山 敏,亀井 譲
- 日形会誌 : 日本形成外科学会会誌 = Journal of Japan Society of Plastic and Reconstructive Surgery 33(7), 519-523, 2013-07-20
- NAID 10031189548
- Hallermann・Streiff 症候群に歯肉腫瘤を伴う先天歯を認めた1例
- 増田 啓次,山座 治義,西垣 奏一郎,小笠原 貴子,大隈 由紀子,柳田 憲一,野中 和明
- 小児歯科学雑誌 51(4), 461-466, 2013
- Hallermann・Streiff 症候群は,骨格形成不全,特有の顔貌,貧毛,皮膚症状,眼症状,歯牙の異常を特徴とする先天性疾患である。我々は,本症候群に先天歯を合併した症例を経験した。先天歯は上顎前歯部に認められ,歯肉腫瘤を伴っていた。また出生直後から経口哺乳が困難で,口から経管栄養チューブが常時挿入されていた。これによる物理的刺激も加わり,先天歯は著しく動揺していた。デンタルエックス線所見で …
- NAID 130005005954
- 下顎腫瘍切除後の小口症に対し顎顔面補綴リハビリテーションを行った1例
- 大木 明子,山越 典雅,高戸 毅
- 顎顔面補綴 = Maxillofacial prosthetics 35(1), 28-35, 2012-06-01
- NAID 10031168135
Related Links
- Definition and history Microstomia is the term used to describe a congenital or acquired reduction in the size of the oral aperture that is severe enough to compromise cosmesis, nutrition, and quality of life. In recent ...
- microstomia [mi″kro-sto´me-ah] abnormally decreased size of the mouth. mi·cro·sto·mi·a (mī'krō-stō'mē-ă), Smallness of the oral fissure or opening. ... Contractions of the facial musculature and other soft tissues cause the patient to ...
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