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「the presence of levulose is the urine; "fructosuria is a harmless condition"」

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出典(authority):フリー百科事典『ウィキペディア(Wikipedia)』「2015/06/13 15:59:12」(JST)

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  • Structures of alternatively spliced isoforms of human ketohexokinase.
  • Trinh CH1, Asipu A, Bonthron DT, Phillips SE.
  • Acta crystallographica. Section D, Biological crystallography.Acta Crystallogr D Biol Crystallogr.2009 Mar;65(Pt 3):201-11. doi: 10.1107/S0907444908041115. Epub 2009 Feb 20.
  • A molecular understanding of the unique aspects of dietary fructose metabolism may be the key to understanding and controlling the current epidemic of fructose-related obesity, diabetes and related adverse metabolic states in Western populations. Fructose catabolism is initiated by its phosphorylati
  • PMID 19237742
  • Doctor, my son is so tired... about a case of hereditary fructose intolerance.
  • Guery MJ1, Douillard C, Marcelli-Tourvieille S, Dobbelaere D, Wemeau JL, Vantyghem MC.
  • Annales d'endocrinologie.Ann Endocrinol (Paris).2007 Dec;68(6):456-9. Epub 2007 Nov 26.
  • We present the case of a 17-year-old male who was diagnosed at birth with hereditary fructose intolerance (HFI). The patient complained of morning-time asthenia and post-prandial drowsiness despite a correct sleep pattern. The physical examination and biological check-up only showed severe vitamin C
  • PMID 18035330
  • Properties of normal and mutant recombinant human ketohexokinases and implications for the pathogenesis of essential fructosuria.
  • Asipu A1, Hayward BE, O'Reilly J, Bonthron DT.
  • Diabetes.Diabetes.2003 Sep;52(9):2426-32.
  • Alternative splicing of the ketohexokinase (fructokinase) gene generates a "central" predominantly hepatic isoform (ketohexokinase-C) and a more widely distributed ketohexokinase-A. Only the abundant hepatic isoform is known to possess activity, and no function is defined for the lower levels of ket
  • PMID 12941785


  • 果糖尿症,Fructosuria,Fructosurie (先天性糖質代謝異常(特集))
  • 加藤 寿一 [他]
  • 小児科診療 29(9), 1073-1080, 1966-09-00
  • NAID 40017892935


fructosuria disturbance of fructose metabolism resulting from a hereditary disorder or intolerance. Normally, fructose is first metabolized in the body to fructose-1-phosphate by a specific organic catalyst or enzyme called fructokinase.
Important It is possible that the main title of the report Fructosuria is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report. ...


La presentación Explore fructosuria in >Essential fructosuria-del metabolismo de la Fructosa Fructosuria Figure 1: The metabolic conversion of Frutas con mayor contenido de fructosa y