先天性胆道拡張症
WordNet
- the state of being stretched beyond normal dimensions (同)distension, distention
- present at birth but not necessarily hereditary; acquired during fetal development (同)inborn, innate
- relating to the bile ducts or the gallbladder
PrepTutorEJDIC
- (病気・身体的欠陥など)生まれつきの,先天的な
UpToDate Contents
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English Journal
- Clinical features of pancreaticobiliary maljunction: update analysis of 2nd Japan-nationwide survey.
- Morine Y, Shimada M, Takamatsu H, Araida T, Endo I, Kubota M, Toki A, Noda T, Matsumura T, Miyakawa S, Ishibashi H, Kamisawa T, Shimada H.SourceJapanese Study Group on Pancreaticobiliary Maljunction, Tokushima, Japan, ymorine@clin.med.tokushima-u.ac.jp.
- Journal of hepato-biliary-pancreatic sciences.J Hepatobiliary Pancreat Sci.2013 Apr 12. [Epub ahead of print]
- INTRODUCTION: Pancreaticobiliary maljunction (PBM) is a congenital anomaly, which can be defined as a union of the pancreatic and biliary ducts located outside off the duodenal wall. We herein investigate clinical features of PBM including as the 2nd report of a Japanese nationwide survey.PATIENTS A
- PMID 23579999
- Tissue culture correlational study of genetic cholangiopathy of autosomal recessive polycystic kidney disease.
- Nakanuma Y, Sato Y, Harada K.SourceDepartment of Human Pathology, Kanazawa University Graduate School of Medicine, Kanazawa, Japan. pbcpsc@kenroku.kanazawa-u.ac.jp
- Methods in molecular biology (Clifton, N.J.).Methods Mol Biol.2013;945:303-18. doi: 10.1007/978-1-62703-125-7_18.
- Cholangiocytes are epithelial cells that line the biliary tract and are also known as biliary epithelial cells (BECs). In vitro culture studies of BECs in correlation with tissue section examination may give us a comprehensive analysis of biliary tract diseases. Herein, we discuss genetic cholangiop
- PMID 23097114
- Duodenal duplication cyst: a potentially malignant disease.
- Seeliger B, Piardi T, Marzano E, Mutter D, Marescaux J, Pessaux P.SourcePôle d'hépato-digestive, Hôpitaux Universitaires de Strasbourg, Université de Strasbourg, Faculté de Médecine, IRCAD/EITS, Institut Hospitalo-Universitaire (IHU) Mix Surg, Strasbourg, France.
- Annals of surgical oncology.Ann Surg Oncol.2012 Nov;19(12):3753-4. doi: 10.1245/s10434-012-2502-4. Epub 2012 Jul 26.
- BACKGROUND: Duodenal duplication cysts constitute a rare congenital anomaly of the gastrointestinal tract. A recent meta-analysis of the literature between 1999 and 2009 reported a total of 47 cases of duodenal duplication cysts.1 These abnormalities are mostly diagnosed in infancy and childhood. In
- PMID 22832999
Japanese Journal
- 症例 膵管非癒合・腹側膵管欠損を伴う先天性胆道拡張症に発生した下部胆管癌の1例
- 吉田 信,高梨 節二,関川 小百合 [他]
- 外科 = Surgey : 臨床雑誌 76(8), 938-941, 2014-08
- NAID 40020162412
- Local Anesthetic Infiltration of the Wound for Postoperative Pain Management in Pediatric Cases
- KIKUCHI TOSHIHIRO,TANABE YUTAKA,KUMAKURA SEIICHIRO,TANAKA HIDEFUMI
- 順天堂醫事雑誌 60(2), 166-169, 2014
- … Case 2 was a 2-year-old female with congenital biliary dilatation. …
- NAID 130004684336
- 副膵管に総胆管が合流した膵胆管合流異常症・完全膵管癒合不全合併の1切除例
- 四倉 正也,鈴木 慶一,金田 宗久,浅沼 史樹,山田 好則
- 日本消化器外科学会雑誌 47(6), 321-328, 2014
- 症例は42歳の女性で，健診の超音波検査で総胆管拡張を指摘され受診した．MRCPで総胆管は30 mmと拡張し，ERCPで主乳頭から造影される腹側膵管は盲端であった．副乳頭からは副膵管および背側膵管が造影され，拡張した総胆管と合流していた．腹側膵管と背側膵管の間に交通は見られなかった．膵・胆管合流異常と完全型膵管癒合不全の合併例と診断し，肝外胆管切除・肝管空腸吻合術を行った．病理組織学的検査所見上， …
- NAID 130004561022
Related Links
- a Department of Pediatric Surgery, Capital Institute of Pediatrics, Beijing 100020, P. R. China b Department of Paediatric Surgery, Monash Children's, Southern Health, Victoria, Department of Paediatrics and Department of Surgery ...
- What most visitors search for before coming to this page What is CBD? One of the definitions of CBD is "congenital biliary dilatation". How to abbreviate congenital biliary dilatation? What is the abbreviation for congenital biliary ...
★リンクテーブル★
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- 英
- congenital biliary dilatation, CBD
- 同
- 先天性総胆管嚢胞 congenital choledochal cyst、先天性総胆管拡張症
[show details]
概念
- 先天性胆道拡張症とは先天的に肝外胆管が嚢状・紡錘状に拡張した疾患。(SSUR.612)
疫学
病態
- 乳幼児期に発症することが多いが、成人期まで無症状のことがある(SSUR.612)
- 10歳までに発症
- 膵胆管合流異常 pancreatico-biliary maljunctionが多くの場合認められる。ほぼ100%らしい。
- 高率に胆管癌を合併。
症候
治療
- 以前は胆嚢の出口？に問題があったと考えられていたので、胆嚢から腸管に胆汁をバイパスする手術が行われていた。
胆管癌の予防
- 高率に胆管癌を合併するために、積極的に胆管切除(嚢腫切除)、胆嚢摘出、胆道再建術(SSUR.612)が必要。
- 手術は、トライツ靭帯より肛門側で空腸を切断し肝臓に吻合。先ほどの空腸と肝臓を吻合した空腸を端側吻合。
参考
- http://www.kms.ac.jp/~hospital/results/sinryouka/p_surgery/index2.html
関連疾患
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- (医)拡張、拡張症
- Physiological, pathological, or artificial enlargement of a cavity, canal, blood vessel, or opening.
dilatation versus dilation
- dilatation: the state of being stretched beyond normal dimensions
- dilation: the act of expanding an aperture; "the dilation of the pupil of the eye"
- 前者は拡張した状態を表す。心拡張(volume loadによる)など。後者は拡張するという動作を表すので、気管拡張薬(bronchial dilatation drugs)、あるいは単語に取り込まれてしまっているが血管拡張薬はvasodilatorなどと使われる。
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- 関
- congenital、congenitally
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- 関
- bile、cholic、gall
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胆管拡張
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