Goodpasture's syndrome

出典: meddic

グッドパスチャー症候群

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出典(authority):フリー百科事典『ウィキペディア(Wikipedia)』「2012/10/26 19:09:35」(JST)

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英文文献

  • Anti-glomerular basement membrane disease treated with mycophenolate mofetil, corticosteroids, and plasmapheresis.
  • Mori M, Nwaogwugwu U, Akers GR, McGill RL.SourceAllegheny General Hospital, West Penn Allegheny Health System, Pittsburgh, and Indiana Regional Medical Center, Indiana, PA, USA.
  • Clinical nephrology.Clin Nephrol.2013 Jul;80(1):67-71.
  • An 18-year-old woman presented with anemia, pulmonary hemorrhage, and necrotizing glomerulonephritis, and was diagnosed with anti-glomerular basement membrane (anti-GBM) disease. Treatment was undertaken with plasma exchange, mycophenolate mofetil and corticosteroids, due to patient refusal of cyclo
  • PMID 23803597
  • Goodpasture's disease: A report of ten cases and a review of the literature.
  • Dammacco F, Battaglia S, Gesualdo L, Racanelli V.SourceDepartment of Internal Medicine and Clinical Oncology, and the Emergency and Organ Transplantation Department, University of Bari Medical School, Bari, Italy. Electronic address: francesco.dammacco@uniba.it.
  • Autoimmunity reviews.Autoimmun Rev.2013 Jun 24. pii: S1568-9972(13)00118-3. doi: 10.1016/j.autrev.2013.06.014. [Epub ahead of print]
  • This review is based on our experience with ten patients diagnosed with Goodpasture's disease (GD). Six of the patients presented with combined renal and pulmonary insufficiencies; in the remaining four patients the clinical findings were limited to renal involvement. Circulating anti-glomerular bas
  • PMID 23806563
  • Regulation of Pathogenic Th17 Cell Differentiation by IL-10 in the Development of Glomerulonephritis.
  • Zhang R, Li Q, Chuang PY, Lu G, Liu R, Yang J, Peng L, Dai Y, Zheng Z, Qi CF, He JC, Xiong H.SourceImmunology Institute, Department of Medicine, Icahn School of Medicine at Mount Sinai, New York, New York.
  • The American journal of pathology.Am J Pathol.2013 Jun 5. pii: S0002-9440(13)00336-2. doi: 10.1016/j.ajpath.2013.05.001. [Epub ahead of print]
  • Although it is clear that T helper (Th)17 cells play a pathologic role in the pathogenesis of several inflammatory diseases, the contribution and regulation of pathogenic Th17 cells in the development of glomerulonephritis are still not fully understood. Herein, we show that IL-10-deficient mice exh
  • PMID 23747510

和文文献

  • 肺胞出血を繰り返すグッドパスチャー症候群患者に対する生体腎移植術の麻酔経験
  • ステロイドが奏効したMPO-ANCA陽性の Goodpasture 症候群の1例
  • 日本呼吸器学会誌 = Annals of the Japanese Respiratory Society 2(1), 18-23, 2013-01-10
  • NAID 10031144753
  • Anti-glomerular basement membrane (anti-GBM) disease accompanied by vasculitis that was not positive for antineutrophil cytoplasmic antibodies to myeloperoxidase and proteinase 3 : a report of two cases and the incidence of anti-GBM disease at one institution
  • Clinical and experimental nephrology 15(4), 504-513, 2011-08-01
  • NAID 10029571698

関連リンク

Goodpasture syndrome is a rare disease that can involve quickly worsening kidney failure and lung disease. Some forms of the disease involve just the lung ... Goodpasture syndrome is an autoimmune disorder. It occurs ...
Goodpasture’s syndrome (also known as Goodpasture’s disease, anti-glomerular basement antibody disease, or anti-GBM disease) is a rare autoimmune disease in which antibodies attack the lungs and kidneys, leading to bleeding ...

関連画像

Goodpasture syndrome pathophysiology Horses and Zebras: Pulmonary-Renal Goodpasture syndrome is a serious Goodpasture syndrome picturesManaging Your Goodpasture's SyndromeGoodpasture’s Syndrome


★リンクテーブル★
リンク元ヒト白血球抗原」「グッドパスチャー症候群」「HLA-DR2
関連記事sing」「syndrome」「S」「ss

ヒト白血球抗原」

  [★]

human leucocyte antigen, HLA
ヒト白血球型抗原HLA抗原 HLA antigenヒト組織適合性白血球抗原 human histocompatibility leukocyteantigen
主要組織適合抗原 MHC ← 免疫との関連はこちらを参照
骨髄バンクHLA抗原

疾患との関連

出典不明

強直性脊椎炎 B27
関節リウマチ DR4
重症筋無力症 DR9,DQ3
尋常性天疱瘡 A26,DR4
バセドウ病 DR5
I型糖尿病(インスリン依存性糖尿病) B54,DR4,DR9,DR53,DQ4
グレーブス病 DR5
ベーチェット病 B51
原田病 DR4,DR53
潰瘍性大腸炎 B52,DR2
クローン病 DR4,DQ3
高安病 B52,DR2,DQ1
バージャー病 B52,DR2,DQ1
ナルコレプシー DR2

first aid step1 2006 p.191

HLA-B27 psoriasis, ankylosing spondylitis, inflammatory bowel disease, Reiter's syndrome.
HLA-B8 Graves' disease, celiac sprue.
HLA-DR2 multiple sclerosis, hay fever, SLE, Goodpasture's syndrome.
HLA-DR3 diabetes mellitus type 1.
HLA-DR4 rheumatoid arthritis, diabetes mellitus type 1.
HLA-DR5 pernicious anemia → B12 deficiency, Hashimoto's thyroiditis.
HLA-DR7 steroid-responsive nephrotic syndrome.

まとめ



グッドパスチャー症候群」

  [★]

Goodpasture syndrome, Goodpasture's syndrome
Goodpasture症候群


  • が冒される
  • 抗基底膜抗体によるII型アレルギー反応が起こる

概念

  • 肺出血と半月体形成を伴う腎炎

病因

  • 抗基底膜抗体(抗糸球体基底膜抗体)が糸球体基底膜と肺胞基底膜とに反応

病理

  • 基底膜に線状の抗体IgGC3の沈着を認める(linear deposition of IgG)
  • 図:BPT. Fig.14-4 B. linear, characteristic of classic anti-GBM antibody GN



HLA-DR2」

  [★]

HLA


sing」

  [★]

  • v.
過去sang-過去分詞sung

WordNet   license wordnet

「to make melodious sounds; "The nightingale was singing"」

WordNet   license wordnet

「deliver by singing; "Sing Christmas carols"」

WordNet   license wordnet

「produce tones with the voice; "She was singing while she was cooking"; "My brother sings very well"」

PrepTutorEJDIC   license prepejdic

「『歌う』;(…に)歌って聞かせる《+『to』(『for』)+『名』》;(楽器に合わせて)歌う《+『to』+『名』》・〈小鳥・虫などが〉『鳴く』,さえずる / 《文》(…を)詩(歌)にする,(詩(歌)を詠んで)賛美する《+『of』+『名』》・〈小川・風・弾丸・湯沸かし・耳などが〉歌うように鳴る・《米語》自白する;密告する・〈歌〉‘を'歌う・《副詞[句]を伴って》歌って…‘を'(…に)する・…‘を'唱える,詠唱する・《文》…‘を'詩(歌)にする,(詩(歌)に詠んで)賛美する・合唱の集い」


syndrome」

  [★]

  • n.

WordNet   license wordnet

「a pattern of symptoms indicative of some disease」

WordNet   license wordnet

「a complex of concurrent things; "every word has a syndrome of meanings"」

PrepTutorEJDIC   license prepejdic

「(疾患の徴候となる一群の)症徴候,症候群 / (事件・社会的状態などのパターンを示す)徴候形態」


S」

  [★]

WordNet   license wordnet

「the 19th letter of the Roman alphabet」
s

PrepTutorEJDIC   license prepejdic

「sulfurの化学記号 / {略}South[ern]」


ss」

  [★]

single strandsingle-strandsingle-stranded





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