Dejerine-Thomas disease

デジュリーヌ・トーマ病

WordNet

1. an impairment of health or a condition of abnormal functioning
2. Welsh poet (1914-1953) (同)Dylan Thomas, Dylan Marlais Thomas
3. a radio broadcast journalist during World War I and World War II noted for his nightly new broadcast (1892-1981) (同)Lowell Thomas, Lowell Jackson Thomas
4. United States socialist who was a candidate for president six times (1884-1968) (同)Norman Thomas, Norman Mattoon Thomas
5. the Apostle who would not believe the resurrection of Jesus until he saw Jesus with his own eyes (同)Saint Thomas, St. Thomas, doubting_Thomas, Thomas the doubting Apostle
6. United States clockmaker who introduced mass production (1785-1859) (同)Seth Thomas
7. caused by or altered by or manifesting disease or pathology; "diseased tonsils"; "a morbid growth"; "pathologic tissue"; "pathological bodily processes" (同)morbid, pathologic, pathological

PrepTutorEJDIC

1. (体の)『病気』,疾患 / (精神・道徳などの)病気,病弊
2. 女性の話術芸人 =diseur
3. 病気にかかった / 病的な,不健全な(morbid)

UpToDate Contents

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• 1. シャルコーマリートゥース病などの一次性の遺伝性運動感覚性ニューロパチー hereditary primary motor sensory neuropathies including charcot marie tooth disease
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• 4. 遺伝性ニューロパチーの概要 overview of hereditary neuropathies
• 5. 慢性膝関節痛または損傷がみられる小児または思春期のアスリートに対するアプローチ approach to the child or adolescent athlete with chronic knee pain or injury

English Journal

• [The cerebellar cortical atrophy syndrome].

• Ponomareva EN, Astapenko AV, Likhachev SA, Ovsiankina GI, Pashko GV, Antonenko AI.
• Zhurnal nevrologii i psikhiatrii imeni S.S. Korsakova / Ministerstvo zdravookhraneniia i meditsinskoĭ promyshlennosti Rossiĭskoĭ Federatsii, Vserossiĭskoe obshchestvo nevrologov [i] Vserossiĭskoe obshchestvo psikhiatrov.Zh Nevrol Psikhiatr Im S S Korsakova.1997;97(9):14-9.
• The results of the observation of 44 patients with cerebellar syndrome of different etiology are presented. Together with careful study of anamnestic and clinical data some additional examinations were performed: senso- and pallesthesiometry, thermovisional investigation, vestibulometry, electroence
• PMID 9410595

• Present criteria for the diagnosis of in vivo of olivopontocerebellar atrophy.

• García de la Rocha ML1, Moreno Martínez JM, Garrido Carrión A, Fernández PM, Martín Araguz A.
• Acta neurologica Scandinavica.Acta Neurol Scand.1988 Mar;77(3):234-8.
• We present 6 cases of olivopontocerebellar atrophy (OPCA) of Dèjérine-Thomas type. The diagnosis was based on an appropriate clinical picture, anomalous brainstem auditory evoked potentials (BAEP) and computerized tomography (CT) and/or magnetic nuclear resonance (MNR) imaging which demonstrated a
• PMID 3163874

• Clinical features of sporadic (Dejerine-Thomas) olivopontocerebellar atrophy.

• Caplan LR.
• Advances in neurology.Adv Neurol.1984;41:217-24.
• PMID 6496227

Related Links

• Dejerine-Thomas syndrome - RightDiagnosis.com

Dejerine-Thomas syndrome symptoms, causes, diagnosis, and treatment information for Dejerine-Thomas syndrome (Dejerine-Sottas disease) with alternative diagnoses, full-text book chapters, misdiagnosis, research treatments ...

• Déjerine-Thomas syndrome | definition of Déjerine-Thomas ...

Déjerine-Thomas syndrome (1) Déjerine-Sottas syndrome, see there. (2) Olivopontocerebellar atrophy, see there. ... Disclaimer All content on this website, including dictionary, thesaurus, literature, geography, and other reference ...

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★リンクテーブル★

リンク元	「オリーブ橋小脳萎縮症」「デジュリーヌ・トーマ病」
関連記事	「disease」

「オリーブ橋小脳萎縮症」

　　[★]

英

olivopontocerebellar atrophy, OPCA, olivopontocerebellar atrophies

同

デジュリーヌ・トーマ病 Dejerine-Thomas disease、オリーブ・橋・小脳萎縮症 olivo-ponto-cerebellar atrophy、オリーブ橋小脳変性症 olivopontocerebellar degeneration

関

spinocerebellar ataxia, SCA1、多系統萎縮症、脊髄小脳変性症

概念

脊髄小脳変性症との関係

• 脊髄小脳変性症 spinocerebellar degeneration SCD

• 1. 孤発性脊髄小脳変性症

• A. 多系統萎縮症 multiple system atrophy MSA

• オリーブ核・橋・小脳萎縮症 OPCA

多系統萎縮症

			小脳失調	自律神経症状	錐体外路症状
オリーブ橋小脳萎縮症	OPCA	MSA-C	○	△	△
Shy-Drager症候群	SDS		△	○	△
線条体黒質変性症	SND	MSA-P	△	△	○

症状

YN.J-124

• 歩行障害→運動失調→平衡障害→構音障害
• 1. 小脳症状
• 2. 錐体路症状
• 3. 錐体外路症状
• 4. 自立心液晶状
• 5. 知能低下

治療

• 酒石酸プロチレリン(TRH)

予後(YN.J-124)

• 緩徐進行。発症後5-10年で死亡

国試

• 099A045

「デジュリーヌ・トーマ病」

　　[★]

英

Dejerine-Thomas disease

関

オリーブ橋小脳萎縮症

「disease」

　　[★]

• n.

疾患：illnessより厳密な概念。「ある臓器に明確な障害が確認され、それによって症状が出ているとはっきり説明できる場合」 (PSY.9)

特定の原因、病態生理、症状、経過、予後、病理組織所見が全てそろった場合 (PSY.9)

• something that is very wrong with people's attitudes, way of life or with society.

関

ail、ailment、disease entity、disorder、ill、illness、malady、sick、sickness

• 注意

disease ≠ illness ≠ disorder